OHVIRA 综合征
介绍最初因发烧和下腹部疼痛到急诊室就诊。随后因超声检查发现左盆腔区域有囊性病变而接受妇产科检查。
患者数据
年龄：10 岁
性别：女
CT
Axial C+ portal
venous phase
Coronal C+ portal
venous phase
Sagittal C+ portal
venous phase
轴向、冠状面和矢状面增强 CT 显示双子宫角（双子宫）、左侧子宫阴道积血（阻塞性半阴道）和左肾发育不全。
病例讨论
OHVIRA（阻塞性半阴道和同侧肾畸形）综合征是一种罕见的先天性疾病，会影响女性生殖和泌尿系统。其特征是存在将阴道分成两部分的隔膜，其中一侧被阻塞，另一侧正常。该病症通常与同侧肾脏异常有关，例如肾发育不全或重复。
OHVIRA 可导致各种症状，例如盆腔疼痛、痛经、反复感染和不孕症。治疗通常包括手术矫正阴道异常和治疗任何相关的肾脏异常。
参考文献
1. Negrão E, Flor-de-Lima B, Dias S, Guimarães L, Madureira A. Herlyn-Werner-Wunderlich Syndrome: A Case Report in a Young Woman, with Literature Review. Radiol Case Rep. 2022;17(6):1991-5. doi:10.1016/j.radcr.2022.03.064 - Pubmed
2. Acién P & Acién M. The Presentation and Management of Complex Female Genital Malformations. Hum Reprod Update. 2016;22(1):48-69. doi:10.1093/humupd/dmv048 - Pubmed
3. Piazza M, Carvalho N, Peixoto A, Urbanetz A. Uterus Didelphys with Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA Syndrome). JBRA Assist Reprod. 2015;19(4):259-62. doi:10.5935/1518-0557.20150049 - Pubmed
4. Oka E, Chiyoda T, Iwata T, Yamagami W, Aoki D. Uterine Cervical Cancer Associated with Obstructed Hemivagina and Ipsilateral Renal Agenesis (OHVIRA) Syndrome: A Case Report and Review of the Literature. Gynecol Oncol Rep. 2020;34:100645. doi:10.1016/j.gore.2020.100645 - Pubmed
5. Chapagain A, Paudel K, Mani Pokhrel S, Prasad Sapkota R. Obstructed Hemivagina and Ipsilateral Renal Agenesis Syndrome: A Case Report. JNMA J Nepal Med Assoc. 2022;60(250):562-4. doi:10.31729/jnma.7444 - Pubmed
页:
[1]